Meetings
2002 Summer School in Primary Immune Deficiency Disorders
Old San Juan, Puerto Rico
August 28-September 1, 2002
Agenda
Friday, August 29, 2002
I. Starting Points: Clinical Evaluations
Francisco A. Bonilla, MD, Children's Hospital, Boston, MA
Case: A boy with recurrent pneumonia and lymphadenitis
Celia Martinez de Cuellar, Instituto de Investigaciones en Ciencias de la Salud
Case: No B Cells
Beatriz Tavares Costa Carvalho, Disciplina de Alergia e Imunologia, Sao Paulo, Brazil
II. Use of
the Laboratory
Thomas A. Fleisher, MD, NIH, Bethesda, MD
Case: Unknown
Jordan Orange, Children's Hospital, Boston, MA
Case: Increased IgE/neutrophil def.
Reza Alizadehfar, Montréal Children's Hospital, Montréal, Canada
III. SCID
and Transplant
Anders
Fasth, MD, The Queen Silvia Children's Hospital, Göteborg, Sweden
Oscar Porras, MD, Hospital Nacional de Ninos, San Jose, Costa Rica
Case: SCID
Margarita Olivares, University of Antigua, Antigua, Columbia
Case: HLH
Jane Sande, University of Alabama-Birmingham
IV. B Cells
Mary Ellen Conley, MD, St Jude Children's Research Hospital, Memphis,
TN
Case: XLA
Andrew Singer, University of Michigan, Ann Arbor, MI
Case: Agamma u chain
Silvia Krasovec, Hospital de Pediatria J.P. Garrahan, Buenos Aires, Argentina
Case: No B Cells
Agnieszka (Agnes) Matczuk, Yale University, New Haven, CT
V. B Cells
Charlotte Cunningham-Rundles, MD, PhD, Mt. Siani Medical Center, New York,
NY
Case: CVID
Theordore Kim, Walter Reed Army Medical Center, Washington, DC
Case: CVID
Cassia Cristina M. Venci Gonzalez, Disciplina de Alergia e Imunologia da Faculdade de Medicina do ABC, São Paulo, Brazil
Saturday, August 30, 2002
VI. Hyper IgM
Hans Ochs, MD, University of Washington, School of Medicine, Seattle,
WA
Case: Hyper IgM
John Williams, Vanderbilt University Medical Center, Nashville, TN
Case: Hyper IgM
Helen Su, NIH, Bethesda, MD
Case: Hyper IgM
Michael Spencer, University of Valparaiso, Quilpu, Chile
VII. Wiskott
Aldrich & varients
Hans Ochs, MD, University of Washington, School of Medicine, Seattle,
WA
VIII. WAS
Treatment Options
Mary Ellen Conley, MD, St Jude Children's Research Hospital, Memphis,
TN
IX. Neutrophils
Steven Holland, MD, NIH, Bethesda, MD
Case: CGD
Curtis Hedberg, Louisiana State University Health Sciences, Shreveport, LA
Case: A Neutrophil Defect?
Maeve O'Connor, National Jewish Medical & Research Center, Denver, CO
Case: Cytokine Receptor Defect
Elizabeth Tepas, Stanford University, Palo Alto, CA
Case: Cytokine Receptor Defect
Sergio Rosensweig, NIH, Bethesda, MD
Case: New Adhesion Defect?
Elena Perez, Children's Hospital of Philadelphia, PA
X. Unknown
Defects / Discussion
Anders Fasth, MD, The Queen Silvia Children's Hospital, Göteborg,
Sweden
Thomas A. Fleisher, MD, NIH, Bethesda, MD
Case: A T Cell Defect
Carla Davis, Baylor College of Medicine, Houston, TXCase: Late dx agamma
Thanai Pongdee, Mayo Clinic, Rochester, MN
XI. Advanced Workup / Treatment - All
XII. Genetic Counseling - All
Sunday, September 1, 2002
XIII. New Defects
Steven Holland, MD, NIH, Bethesda, MD
Case: Unknown Defect
Gulbu Uzel, Department of Laborartory Medicine, NIH, Bethesda, MD
Case: MBL/neutrophil
Rajivi Rucker, All Children's Hospital, St. Petersburg, FL
IXX. New
Defects & More
Hans Ochs, MD, University of Washington, School of Medicine, Seattle,
WA
Fasth, MD, The Queen Silvia Children's Hospital, Göteborg, Sweden
Case: XLP
Troy Torgerson, University of Washington, School of Medicine, Seattle, WA
Case: IPEX
Marc Reidl, UCLA Medical Center, Los Angeles, CA













